TY - JOUR
T1 - The status of polycystic liver disease in Japan
T2 - A questionnaire survey of patients
AU - Ogawa, Koichi
AU - Fukunaga, Kiyoshi
AU - Takeuchi, Tomoyo
AU - Kawagishi, Naoki
AU - Kudo, Masatoshi
AU - Ohkouchi, Nobuhiro
N1 - Copyright:
Copyright 2018 Elsevier B.V., All rights reserved.
PY - 2011
Y1 - 2011
N2 - Polycystic liver disease (PLD) is genetic disorder characterized by the progressive development of multiple liver cysts. Because of rarity of PLD, therapeutic consensus is controversial. The aim of this study was to investigate a situation of PLD treatment by a questionnaire survey. In this study, 422 patients with PLD participated and 223 patients underwent treatment the most common symptom was abdominal distension (73%). The treatments were performed as follows; percutaneous aspiration in 27% of patients, liver resection in 12%, cyst fenestration in 9%, and liver transplantation in 3%. The efficacies of these treatments were recognized in 77%, 96%, 92%, and 100% of each patient respectively. Because of no effect of primary therapy, additional treatment was performed in only 4.3% of patients. In general, the choice of primary treatment for PLD was considered reasonable and proper, in Japan.
AB - Polycystic liver disease (PLD) is genetic disorder characterized by the progressive development of multiple liver cysts. Because of rarity of PLD, therapeutic consensus is controversial. The aim of this study was to investigate a situation of PLD treatment by a questionnaire survey. In this study, 422 patients with PLD participated and 223 patients underwent treatment the most common symptom was abdominal distension (73%). The treatments were performed as follows; percutaneous aspiration in 27% of patients, liver resection in 12%, cyst fenestration in 9%, and liver transplantation in 3%. The efficacies of these treatments were recognized in 77%, 96%, 92%, and 100% of each patient respectively. Because of no effect of primary therapy, additional treatment was performed in only 4.3% of patients. In general, the choice of primary treatment for PLD was considered reasonable and proper, in Japan.
KW - Fenestration
KW - Liver resection
KW - Liver transplantation transcatheter hepatic artery embolization
KW - Polycystic liver disease
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U2 - 10.2957/kanzo.52.709
DO - 10.2957/kanzo.52.709
M3 - Article
AN - SCOPUS:82755170457
VL - 52
SP - 709
EP - 715
JO - Acta Hepatologica Japonica
JF - Acta Hepatologica Japonica
SN - 0451-4203
IS - 11
ER -