TY - JOUR
T1 - Japanese Biliary Atresia Registry, 1989 to 1994
AU - Ibrahim, Mohamed
AU - Miyano, Takeshi
AU - Ohi, Ryoji
AU - Saeki, Morihiro
AU - Shiraki, Kazuo
AU - Tanaka, Koichi
AU - Kamiyama, Takamichi
AU - Nio, Masaki
N1 - Copyright:
Copyright 2017 Elsevier B.V., All rights reserved.
PY - 1997/1
Y1 - 1997/1
N2 - The Japanese Biliary Atresia Society founded in 1980 for the aim of investigations of all aspects of biliary atresia (BA), started a nationwide registry of BA patients in 1989. A total of 626 cases were registered from 1989 to 1994. The male to female ratio was 0.58. Corrective surgery was performed in 603 patients. Regarding the type of obstruction, 63 cases were Type I, atresia of the common bile duct, 9 were Type II, atresia of the hepatic ducts, and 543 were Type III, atresia of the porta hepatis. As initial corrective procedures, original Roux-en Y, Suruga II and Roux-en Y with intestinal valve were mainly employed. Jaundice cleared in 346 patients (57%) and decreased in 131, while it persisted in 120. The 5-year-follow-up showed that 34 patients, 49% of the patients who were followed up, were alive without jaundice, while 28 (41%) are dead. Thirty five, 33% of the patients who were entered to the Registry, were lost to follow-up.
AB - The Japanese Biliary Atresia Society founded in 1980 for the aim of investigations of all aspects of biliary atresia (BA), started a nationwide registry of BA patients in 1989. A total of 626 cases were registered from 1989 to 1994. The male to female ratio was 0.58. Corrective surgery was performed in 603 patients. Regarding the type of obstruction, 63 cases were Type I, atresia of the common bile duct, 9 were Type II, atresia of the hepatic ducts, and 543 were Type III, atresia of the porta hepatis. As initial corrective procedures, original Roux-en Y, Suruga II and Roux-en Y with intestinal valve were mainly employed. Jaundice cleared in 346 patients (57%) and decreased in 131, while it persisted in 120. The 5-year-follow-up showed that 34 patients, 49% of the patients who were followed up, were alive without jaundice, while 28 (41%) are dead. Thirty five, 33% of the patients who were entered to the Registry, were lost to follow-up.
KW - Biliary atresia
KW - Japan
KW - Registry
UR - http://www.scopus.com/inward/record.url?scp=0030633318&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=0030633318&partnerID=8YFLogxK
U2 - 10.1620/tjem.181.85
DO - 10.1620/tjem.181.85
M3 - Article
C2 - 9149343
AN - SCOPUS:0030633318
VL - 181
SP - 85
EP - 95
JO - Tohoku Journal of Experimental Medicine
JF - Tohoku Journal of Experimental Medicine
SN - 0040-8727
IS - 1
ER -