Improvement of Action Myoclonus in a Patient with Dentatorubral-Pallidoluysian Atrophy by Piracetam

Mieko Hirose, Hiroyuki Yokoyama, Rie Noguchi, Kazuhiro Haginoya, Masashi Aoki, Kazuie Iinuma

Research output: Contribution to journalArticlepeer-review

1 Citation (Scopus)

Abstract

We report a 13-year-old girl with dentatorubal-pallidoluysian atrophy (DRPLA), presenting clinically as progressive myoclonic epilepsy. The action myoclonus, which severely impaired her daily life, was markedly improved by administration of piracetam, a drug reportedly useful for myoclonus of cortical origin. In our case, piracetam effectively suppressed severe subcortical myoclonus of DRPLA, suggesting that the drug may be useful in the treatment of both cortical, and subcortical myoclonus.

Original languageEnglish
Pages (from-to)75-79
Number of pages5
JournalNo To Hattatsu
Volume36
Issue number1
Publication statusPublished - 2004

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Clinical Neurology

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