Congenital cholesteatoma of mastoid region manifesting as acute mastoiditis: Case report and literature review

H. Hidaka, E. Ishida, K. Kaku, H. Nishikawa, T. Kobayashi

Research output: Contribution to journalReview articlepeer-review

10 Citations (Scopus)

Abstract

Objectives: We report an extremely rare case of congenital cholesteatoma of the mastoid region, presenting as acute mastoiditis. We also review the 16 previously reported cases of congenital cholesteatoma of the mastoid region.Case report: A 65-year-old man presented with left-sided, post-auricular swelling and pain. Acute mastoiditis was diagnosed, with computed tomography demonstrating destruction of the bony plates of the posterior cranial fossa and sigmoid sinus. Initial surgery revealed a cholesteatoma in the mastoid, with no extension into the aditus ad antrum or attic. These findings were confirmed by pathological and immunohistochemical analysis of the surgical specimen, the latter using involucrin. The cholesteatoma matrix was completely removed in a second operation.Conclusions: Including this case, only four of the 17 reported cases of congenital cholesteatoma of the mastoid region showed post-auricular pain or swelling, indicating acute mastoiditis. Clinicians should bear in mind that congenital cholesteatoma may be present in patients presenting with mastoiditis, particularly adults.

Original languageEnglish
Pages (from-to)810-815
Number of pages6
JournalJournal of Laryngology and Otology
Volume124
Issue number7
DOIs
Publication statusPublished - 2010 Jul

Keywords

  • Cholesteatoma
  • Congenital
  • Mastoiditis
  • Temporal Bone

ASJC Scopus subject areas

  • Otorhinolaryngology

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