Airway management in a patient with Williams syndrome

Akihiro Kanaya, Tadanobu Yasuda, Akiko Kojima, Toshio Saishu, Shin Kurosawa

    Research output: Contribution to journalArticlepeer-review

    Abstract

    Williams syndrome is characterized by the triad of supravalvular aortic stenosis (SAS), mental retardation and elfin facies. Generally, difficult airway is expected in patients with Williams syndrome by characteristic face. A 26-year-old female with Williams syndrome was scheduled for abdominal myomectomy under general anesthesia. Difficult mask ventilation and tracheal intubation were anticipated because of micrognathia, mandibular retrusion, and a Mallanpati classIII airway. Before induction of anesthesia the patient breathed 100% oxygen for 3 minutes. Anesthesia was induced and maintained with propofol, remifentanil and rocuronium bromide. Mask ventilation was easily performed. The direct laryngoscopy view was Cormack grade I and there was no difficulty in the tracheal intubation. After induction of anesthesia, anesthetic course was uneventful. According to the most previous clinical reports in patients with Williams syndrome in Japan, mask ventilation and tracheal intubation were performed easily contrary to preoperative airway assessment. In view of SAS, mental retardation, airway deformity and airway assessment in previous clinical reports, we should select the optimal strategy for airway management in patients with Williams syndrome.

    Original languageEnglish
    Pages (from-to)1176-1179
    Number of pages4
    JournalJapanese Journal of Anesthesiology
    Volume60
    Issue number10
    Publication statusPublished - 2011 Oct 10

    Keywords

    • Airway management
    • General anesthesia
    • Williams syndrome

    ASJC Scopus subject areas

    • Anesthesiology and Pain Medicine

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