A rare craniofacial cleft; Tessier Type VI-VII Cleft combination associated with abnormal cleft palate

Congenital intermaxillary fusion is a rare anomaly. Combination of the anomaly with any type of facial cleft is extremely rare. As a whole, facial clefts occur with an incidence from 1.43 to 4.85 per 100,000 births, and the pathogenesis behind the formation of this anomaly is unknown. Many theories, such as the failure of the processes to achieve contact central disorganization of the neural crest, external pressures, oligohydramnios, amniotic bands, and hematoma have been proposed. Therefore, surgical correction is an extremely difficult approach in the field of pediatric plastic surgery. In a woman of 37weeks and 2634 g of gestation at birth, we diagnosed Tessier Type VI-VII Cleft combination, associated with abnormal cleft palate on the right side. We achieved a satisfactory result after treatment of this case using a similar treatment approach as for cleft lip and palate.