A case of Usher syndrome type 3 with sudden hearing loss

T. Oshima

Research output: Contribution to journalArticlepeer-review


Usher syndrome is characterized by bilateral sensorineural hearing loss with retinitis pigmentosa and has an autosomal recessive mode of inheritance. Usher syndrome has been decided into two major clinical types, type 1 and 2. The existence of the third type, which is distinguished from type 1 and 2 by the progressive nature of the hearing loss, has been suggested. A 20-year old man presented with progressive sensorineural hearing loss. After 6 years, he has been suffering from retinis pigmentosa. According to the combination of visual and hearing disorders, he was diagnosed as usher syndrome type 3.

Original languageEnglish
Pages (from-to)484-487
Number of pages4
JournalOtolaryngology - Head and Neck Surgery (Tokyo)
Issue number6
Publication statusPublished - 1996 Jan 1

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Surgery


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