A case of congenital unilateral maxillo-mandibular bony fusion in an 8-year-old girl

Satoko Koeda; Takahiro Suzuki; Hitoshi Nei; Hanae Inahara; Yoko Takata; Satoshi Goto; Hiroshi Nagasaka; Hiroshi Kawamura

doi:10.1016/j.ajoms.2010.06.003

A case of congenital unilateral maxillo-mandibular bony fusion in an 8-year-old girl

Satoko Koeda, Takahiro Suzuki, Hitoshi Nei, Hanae Inahara, Yoko Takata, Satoshi Goto, Hiroshi Nagasaka, Hiroshi Kawamura

Research output: Contribution to journal › Article › peer-review

3 Citations (Scopus)

Abstract

Congenital fusion of the mandible to maxilla can involve soft tissue (synechiae) or bone (syngnathia). Congenital synechiae has been widely reported, whereas congenital syngnathia is rare. Syngnathia severely limits mouth opening. To improve airway control and prevent feeding handicaps, surgical division of the bony fusion or breakdown of the adhesions is recommended within the first few days of life. We described an 8-year-old girl who had unilateral syngnathia with micromandible, reactive coronoid process hyperplasia, cleft palate and congenital corneal opacity. She first underwent surgical treatment to improve jaw function at the age of 8 years. Delayed surgery slightly improved restricted mouth opening.

Original language	English
Pages (from-to)	220-224
Number of pages	5
Journal	Asian Journal of Oral and Maxillofacial Surgery
Volume	22
Issue number	4
DOIs	https://doi.org/10.1016/j.ajoms.2010.06.003
Publication status	Published - 2010 Oct 1

Keywords

Cleft palate
Corneal opacity
Micromandible
Reactive coronoid process hyperplasia
Syngnathia

ASJC Scopus subject areas

Surgery
Oral Surgery
Orthopedics and Sports Medicine

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10.1016/j.ajoms.2010.06.003

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title = "A case of congenital unilateral maxillo-mandibular bony fusion in an 8-year-old girl",

abstract = "Congenital fusion of the mandible to maxilla can involve soft tissue (synechiae) or bone (syngnathia). Congenital synechiae has been widely reported, whereas congenital syngnathia is rare. Syngnathia severely limits mouth opening. To improve airway control and prevent feeding handicaps, surgical division of the bony fusion or breakdown of the adhesions is recommended within the first few days of life. We described an 8-year-old girl who had unilateral syngnathia with micromandible, reactive coronoid process hyperplasia, cleft palate and congenital corneal opacity. She first underwent surgical treatment to improve jaw function at the age of 8 years. Delayed surgery slightly improved restricted mouth opening.",

keywords = "Cleft palate, Corneal opacity, Micromandible, Reactive coronoid process hyperplasia, Syngnathia",

author = "Satoko Koeda and Takahiro Suzuki and Hitoshi Nei and Hanae Inahara and Yoko Takata and Satoshi Goto and Hiroshi Nagasaka and Hiroshi Kawamura",

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AU - Koeda, Satoko

AU - Suzuki, Takahiro

AU - Nei, Hitoshi

AU - Inahara, Hanae

AU - Takata, Yoko

AU - Goto, Satoshi

AU - Nagasaka, Hiroshi

AU - Kawamura, Hiroshi

PY - 2010/10/1

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N2 - Congenital fusion of the mandible to maxilla can involve soft tissue (synechiae) or bone (syngnathia). Congenital synechiae has been widely reported, whereas congenital syngnathia is rare. Syngnathia severely limits mouth opening. To improve airway control and prevent feeding handicaps, surgical division of the bony fusion or breakdown of the adhesions is recommended within the first few days of life. We described an 8-year-old girl who had unilateral syngnathia with micromandible, reactive coronoid process hyperplasia, cleft palate and congenital corneal opacity. She first underwent surgical treatment to improve jaw function at the age of 8 years. Delayed surgery slightly improved restricted mouth opening.

AB - Congenital fusion of the mandible to maxilla can involve soft tissue (synechiae) or bone (syngnathia). Congenital synechiae has been widely reported, whereas congenital syngnathia is rare. Syngnathia severely limits mouth opening. To improve airway control and prevent feeding handicaps, surgical division of the bony fusion or breakdown of the adhesions is recommended within the first few days of life. We described an 8-year-old girl who had unilateral syngnathia with micromandible, reactive coronoid process hyperplasia, cleft palate and congenital corneal opacity. She first underwent surgical treatment to improve jaw function at the age of 8 years. Delayed surgery slightly improved restricted mouth opening.

KW - Cleft palate

KW - Corneal opacity

KW - Micromandible

KW - Reactive coronoid process hyperplasia

KW - Syngnathia

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A case of congenital unilateral maxillo-mandibular bony fusion in an 8-year-old girl

Abstract

Keywords

ASJC Scopus subject areas

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