We report a case of chronic intestinal pseudo-obstruction (CIP) due to primary amyloidosis. A 56-year-old man with abdominal distention and diagnosed with idiopathic CIP underwent emergency surgery after the duodenum was thought to have been perforated during re-insertion of a long intestinal tube. Although no perforation was detected in the duodenum or small intestine, the jejuoileal intestinal wall was extremely fragile, and gut-handling caused multiple perforations, necessitating resection of the small intestine for 300cm and end je-junostomy. Pathological examination showed CIP secondary to primary amyloidosis, which caused the men's death six months later. The prognosis for CIP secondary to primary amyloidosis is dismal, with surgical intervention a last-ditch effort because destruction of the intestinal wall is go rapid.
- Chronic intestinal pseudo-obstruction
- Primary amyloidosis
ASJC Scopus subject areas